Retroperitoneal Fibrosis

Diagnostic Challenge and Imaging Features

Abstract

Retroperitoneal fibrosis (RPF) is a rare condition with an incidence of 1.3 per 100 000 population with a peak age of onset at 40 – 65 years old. The idiopathic form of RPF, also known as Ormond’s disease, is more common and makes up about 75% of the case. Here, we are presenting a case of a woman who was referred to our center due to worsening serum creatinine and was diagnosed with retroperitoneal fibrosis. This case has been taken up due to the rarity of the case and to discuss the radiological appearance specifically the CT appearance of retroperitoneal fibrosis. We have also discussed methods to differentiate between primary and secondary retroperitoneal fibrosis specifically based on CT findings. This is to provide guidance for the diagnosis and prompt management of cases, especially in district hospitals with no advanced diagnostic equipment such as MRI or the ability to biopsy.